Haemophagocytic lymphohistiocytosis

Haemophagocytic Lymphohistiocytosis (HLH) in children - Histio UK

HLH can be likened to a very severe form of inflammation which the body is unable to switch off. It results from an uncontrolled increase in the numbers of ...

Lymphohistiocytosis (Hemophagocytic Lymphohistiocytosis) Clinical ...

Hemophagocytic lymphohistiocytosis (HLH) is a rare but potentially fatal disease of normal but overactive histiocytes and lymphocytes that ...

Haemophagocytic Lymphohistiocytosis (HLH) or Macrophage ...

HLH is the coexistence of immune dysregulation and unchecked inflammation and is a rare and often life threatening condition.

Haemophagocytic syndromes: the importance of early diagnosis ...

At onset, the clinical manifestations of HLH are those of any severe infectious disease. It is characterised by prolonged high fever and progressive ...

Familial hemophagocytic lymphohistiocytosis - Orphanet

Familial Hemophagocytic lymphohistiocytosis (FHL) is a rare primary immunodeficiency characterized by a macrophage activation syndrome (see this ...

Advances in the diagnosis and management of haemophagocytic ...

Haemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome, triggered by the excessive stimulation of lymphocytes and macrophages producing ...

Genetics and pathophysiology of haemophagocytic ...

Haemophagocytic lymphohistiocytosis (HLH) represents a life-threatening hyperinflammatory syndrome. Familial studies have established ...

Hemophagocytic Lymphohistiocytosis: A Primer for Radiologists | AJR

Clinical Features and Imaging Findings. Patients with HLH often present with a critically ill clinical picture similar to that of sepsis. The most common ...

Lymphoma-associated hemophagocytic lymphohistiocytosis (LA-HLH)

Hemophagocytic lymphohistiocytosis (HLH) is a severe hyperinflammatory syndrome driven by pathologic activation of cytotoxic T-lymphocytes ...

Haemophagocytic lymphohistiocytosis (HLH) in patients with large B ...

HLH is a rare but serious complication of chimeric antigen receptor (CAR) T cell therapy, characterized by severe immune activation, and immune mediated multi- ...

Hemophagocytic lymphohistiocytosis: a review inspired by the ...

This paper aims to review the pathogenesis and the clinical picture of HLH, and its severe complication, the cytokine storm, with a special emphasis on the ...

Haemophagocytic lymphohistiocytosis in adult critical care

Abstract. Haemophagocytic lymphohistiocytosis (HLH) is a syndrome of severe immune dysregulation, characterised by extreme inflammation, fever, ...

Hemophagocytic Lymphohistiocytosis

Familial haemophagocytic lymphohistiocytosis: advances in the genetic basis, diagnosis and management.

Haemophagocytic lymphohistiocytosis (HLH) in human ...

HLH is a hyper-immune condition secondary to malignancy, infection or auto-immune conditions. HLH in patients with human immunodeficiency virus infection (HIV)

Adult haemophagocytic lymphohistiocytosis: a review | QJM

Haemophagocytic lymphohistiocytosis (HLH) is a rare disorder characterized by intense hyperimmune response and uncontrolled release of inflammatory cytokines.

Haemophagocytic lymphohistiocytosis in patients treated with ...

Immune checkpoint inhibitor (ICI) use in clinical practice has unravelled a spectrum of immune-related adverse events (irAEs) due to immune ...

Neonatal Hemophagocytic Lymphohistiocytosis | NeoReviews

Conclusion. Neonatal presentation of HLH is extremely rare. Clinicians should consider HLH in their differential diagnosis in neonates with ...

Haemophagocytic Lymphohistiocytosis (HLH) - GIRFT

Haemophagocytic Lymphohistiocytosis (HLH) is a devastating syndrome with uncontrolled activation of the immune system leading to ...

Current status of the diagnosis and treatment of hemophagocytic ...

Hemophagocytic lymphohistiocytosis (HLH) is a group of diseases belonging to histiocytosis syndrome [1]. It manifests as high fever and ...

Adult onset haemophagocytic lymphohistiocytosis prognosis is ...

Haemophagocytic lymphohistiocytosis (HLH) is a rare clinical syndrome characterised by activation of the mononuclear phagocytic system, and ...