Assessing upper limb function in nonambulant SMA patients

Assessing upper limb function in nonambulant SMA patients - PubMed

We report the development of a module specifically designed for assessing upper limb function in nonambulant SMA patients, including young children and ...

The final version, called Upper Limb Module (ULM) includes 9 items that can be performed using very little equipment (pencil, coin, plastic cup, button, lamp, ...

Assessing upper limb function in nonambulant SMA patients

The upper limb scores had a good correlation with the Hammersmith Functional Motor Scale, r=0.75, but the upper limb function did not always strictly follow the ...

Assessing upper limb function in nonambulant SMA patients

The upper limb scores had a good correlation with the Hammersmith Functional Motor Scale, r = 0.75, but the upper limb function did not always strictly follow ...

Improved upper limb function in non-ambulant children with SMA ...

Results: Data from 256 non-ambulant, pediatric patients with SMA were included in the data analysis. Improvements in motor function were more ...

Assessment of the upper limb function, strength, and mobility in ...

SMA in children is classified into three main disease subtypes, characterized by the age of onset and highest motor milestone achieved. SMA Type ...

Assessing upper limb function in nonambulant SMA patients ...

Abstract We report the development of a module specifically designed for assessing upper limb function in nonambulant SMA patients, including young children ...

Improved upper limb function in non-ambulant children with SMA ...

Improvements in motor function were more prominent in upper limb: 32.4% of patients experienced clinically meaningful improvements in RULM and ...

Assessing upper limb function in nonambulant SMA patients ...

Assessing upper limb function in nonambulant SMA patients: Development of a new module. E. Mazzone, F. Bianco, D. Martinelli, A. M. Glanzman, S. Messina ...

Upper limb module in non-ambulant patients with spinal muscular ...

In contrast, the HFMS appeared to be less sensitive to record activities in the very weak patients, in axial and upper limb activities could be assessed using ...

Upper Limb Evaluation and One-Year Follow Up of Non-Ambulant ...

Assessment of the upper limb strength in non-ambulant neuromuscular patients remains challenging. Although potential outcome measures have been reported, ...

Examination of Upper Limb Function and the Relationship with ...

The HFMSE scale is a validated tool to evaluate the gross motor function of SMA patients [13,14]. The RULM scale is used to determine the upper limb function.

Assessing upper limb function in nonambulant SMA patients

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Assessing upper limb function in nonambulant SMA patients ...

Assessing upper limb function in nonambulant SMA patients: development of a new module.-article.

Assessment of the upper limb function, strength, and mobility in ...

Upper limb function, strength, and hand/finger mobility in treatment-naïve children with spinal muscular atrophy Types 2 and 3 were assessed ...

Innovative methods to assess upper limb strength and function in ...

Egen Klassification scale has been validated in spinal muscular atrophy and DMD, and is specifically designed for non-ambulant patients [15]. Reliability is ...

Systematic Review of Motor Function Scales and Patient-Reported ...

Spinal muscular atrophy (SMA) is an autosomal recessive disease caused by homozygous deletion or loss-of-function mutation in the survival motor neuron 1 (SMN1) ...

Quantitative description of upper extremity function and activity of ...

Therefore, we aimed to measure physiologic UE function of SMA patients with different functional abilities and evaluate the relation between ...

Respiratory, Upper Limb Function Declines After Loss of Ambulation ...

Ambulatory patients with SMA did not benefit differently from therapy compared to those who were non-ambulatory. Ambulatory patients achieved ...

[PDF] Revised upper limb module for spinal muscular atrophy

The results confirm that the Revised Upper Limb Module explores a wide range of functional abilities and can be used in ambulant and non‐ambulant patients ...