a prognostic study in paediatric pulmonary hypertension

Prognostic factors in pediatric pulmonary arterial hypertension

The aim of this study was to identify and evaluate prognostic factors in pediatric PAH by a systematic review of the literature and to summarize ...

3D echocardiographic evaluation of right ventricular function and ...

Paediatric pulmonary hypertension (PH) is a progressive disease that results in right ventricular (RV) dysfunction; RV function is an important ...

Prognostic biomarkers in pediatric pulmonary arterial hypertension

The main reasons are a lack of disease specificity, contradictory study findings and unpredictable treatment effects. A study on ET-1 in pediatric PAH did not ...

Prognostic Value of Transthoracic Echocardiography in Children ...

Pulmonary arterial hypertension (PAH) represents a rare but life‐threatening chronic condition in children. ... Despite major advances in drug ...

Prognostic factors in pediatric pulmonary arterial hypertension

This systematic review combined with separate meta-analyses shows that WHO-FC, (NT-pro)BNP, mRAP, PVRi, cardiac index and acute vasodilator response are ...

Prognostic Value of Serial Risk Stratification in Adult and Pediatric ...

This systematic review aims to report the prognostic value of serial risk stratification in adult and pediatric pulmonary arterial hypertension.

Paediatric pulmonary hypertension: monitoring progress and ...

The international TOPP registry will provide a valuable insight, but this must be complemented by research and development of adapted paediatric therapies.

Pulmonary hypertension in children: Management and prognosis

Outline · SUMMARY AND RECOMMENDATIONS · INTRODUCTION · TERMINOLOGY · MULTIDISCIPLINARY APPROACH · TREATMENT OF UNDERLYING DISORDERS · SUPPORTIVE ...

Echocardiographic Changes and Long-Term Clinical Outcomes in ...

In children, pulmonary arterial hypertension (PAH) is a rare but progressive disease that ultimately leads to right ventricular failure and ...

Prognostic Value of Early Risk Stratification in Pediatric Pulmonary ...

Survival analysis showed that PAH etiology might be an important determinant in pediatric PAH risk stratification. We confirmed that PVRI has predictive value ...

Paediatric pulmonary arterial hypertension: updates on definition ...

Due to variability in pulmonary haemodynamics during post-natal transition, paediatric PH has been defined as mPAP ≥25 mmHg after 3 months of age. In paediatric ...

The Pulmonary Artery Pulsatility Index Provides No Additional ...

This study had several strengths. First, it is a large, well and consistently maintained study population for the rare disease of pediatric PAH. In this study, ...

Idiopathic Pulmonary Arterial Hypertension and ... - Frontiers

This study describes and compares clinical features of pediatric IPAH and PAH-CHD in a single center of China during an 11-year period and explores the ...

3D echocardiographic evaluation of right ventricular function and ...

To evaluate right ventricular functional indices using 3D echocardiography (3DE) between normal children and paediatric pulmonary hypertension ( ...

American Journal of Respiratory and Critical Care Medicine

The prognostic value of CPET parameters is now well established in adult PAH (6, 7). In pediatric PAH, it has been shown that CPET parameters correlate with ...

Invasive haemodynamics predict outcomes in paediatric pulmonary ...

Little is known about the predictive value of invasive haemodynamic indices for long-term outcomes in children with pulmonary artery ...

Diagnostics, monitoring and outpatient care in children ... - BMJ Heart

Pulmonary hypertension (PH) is a condition of multiple aetiologies with underestimated prevalence and incidence. Indeed, despite access to modern therapies, ...

Embracing the challenges of neonatal and paediatric pulmonary ...

Risk assessment plays a crucial role in the current management of children with PAH. Risk assessment is used to determine the patient's risk for adverse outcome ...

Pediatric Pulmonary Hypertension - JACC Journals

Additionally, a retrospective study from the United Kingdom has shown the survival in 216 children with IPAH and APAH-CHD (1). The survival rates of IPAH were ...

Pediatric Idiopathic Pulmonary Artery Hypertension

Survival has improved, although morbidity and mortality remain significant. In 2009, the United Kingdom Pulmonary Hypertension Service for ...